Diagnosis

Acute invasive fungal sinusitis

An invasive fungal sinus infection that usually occurs in an immunocompromised (HIV/AIDS, diabetic) host. It is a medical emergency with high mortality rate (50-80%) [abt].

Also known as: Acute invasive fungal rhinosinusitis, Fulminant invasive fungal sinusitis, Mucormycosis, Zygomycosis

Etiology

Cause [abt]

Pathophysiology [vgo]

The immune fitness of the individual often plays a more central role in determining whether those atmospheric fungi lead to the pathology of the sinuses or not

Risk factors

Classification [vgo]

  1. Non-invasive fungal sinusitis:

    • Fungal ball

    • Saprophytic fungal sinusitis

    • Allergic fungal rhinosinusitis

  2. Invasive fungal sinusitis:

    • Acute invasive rhinosinusitis

    • Chronic invasive rhinosinusitis

    • Granulomatous invasive sinusitis

Epidemiology

Incidence per 100.000 [7ru]

Epidemiology chart for Incidence

Symptoms & findings

Symptoms

Anopsia, Anosmia, Epistaxis, Fever, Headache, Nasal congestion, Ophthalmoplegia, Post-nasal drip, Pruritus, Rhinorrhea, Sneezing

Clinical findings

None listed.

Anamneses

None listed.

Localized findings

Pain
Radiates
Maxillofacial
Onset
Gradual (days)
Pattern
Constant
Quality
Pressing
Severity
Moderate (4-7)Severe (8-10)
Rash
Radiates
Regio nasalis
Lesion type
NecrosisUlcer
Swelling
Radiates
MaxillofacialRegio orbitalis
Onset
Gradual (days)
Pattern
Constant

Approach

Treatment

  1. Reversal of immunosuppression

  2. Immune-stimulating therapies / Fungal immunotherapy

  3. Surgery: débridement of necrotic tissue and to clear the burden of fungal elements [vgo]

  4. Oral corticosteroids

  5. Antifungal therapy (Amphotericin B if Mucor species and Aspergillus)

Differential diagnoses

Acute sinusitis, Allergic rhinosinusitis, Cancer, Chronic sinusitis, Immunodeficiency, Sarcoidosis, Wegener's granulomatosis


References

[1] Deutsch PG, Whittaker J, Prasad S. Invasive and Non-Invasive Fungal Rhinosinusitis-A Review and Update of the Evidence. Medicina (Kaunas). 2019 Jun 28;55(7):319.

[2] Akhondi H, Woldemariam B, Rajasurya V. Fungal Sinusitis. [Updated 2023 Jul 3]. In: StatPearls [Internet]. Treasure Island (FL): StatPearls Publishing; 2025 Jan-. Available from: https://www.ncbi.nlm.nih.gov/books/NBK551496/

[3] Shintani-Smith et al. Acute invasive fungal sinusitis: Epidemiology and outcomes in the United States. Int Forum Allergy Rhinol. 2022 Feb;12(2):233-236.

[4] Gonzalez et al. Acute Invasive Fungal Sinusitis: A 30-Year Review of Pathology Practice and Possible Utility of the DiffQuik® Stain. Head Neck Pathol. 2021 Sep;15(3):852-858.

[5] Turner et al. Survival outcomes in acute invasive fungal sinusitis: a systematic review and quantitative synthesis of published evidence. Laryngoscope. 2013 May;123(5):1112-8.

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